Unit 4: Refractive Error

Keratoconus is a bilateral (85% of cases) acquired, corneal collagen disorder , in which the cornea, thins and distorts. Peak onset is usually in late teens to twenties.

Systemic associations include:

  • Downs syndrome
  • Ehlers-Danlos syndrome
  • Marfans syndrome

Signs

  • Increase in corneal astigmatism and often myopia
  • Abnormal retinoscopy reflex (appears like a oil droplet)
  • Retinoscope reflex shows scissors movement
  • Central corneal thinning and conical shape (steepening of corneal curvature)
  • Bulging of the lower lid on down gaze
  • Vertical lines in the corneal stroma (striae)

Management

  • Contact lenses, fit with Rigid gas permeable for optimum visual acuity, often better than spectacles.
  • Often photorefractive surgery is contraindicated
  • Can require corneal graft in late stages if scarring present
  • Monitor regularly for progression.